Kaposifrom Hemangioendothelioma of the Skull in a 3 Year--Old Boy

Authors

  • Ahmad Faramarzi Dept. Of pathology. Kermanshah University of Medical sciences, Kermanshah, Iran
  • Etrat Javadi Rad Dept. Of pathology. Kermanshah University of Medical sciences, Kermanshah, Iran
  • Seyed Hamid Madani Dept. Of pathology. Kermanshah University of Medical sciences, Kermanshah, Iran
Abstract:

  Kaposiform hemangioendothelioma (KHE) appears as a single lesion at birth or early infancy in an equal sex ratio. A rare aggressive vascular proliferation has been recognized as a separate entity from other childhood vascular neoplasm. A 3-year-old Iranian boy with a rapidly enlarging mass in his (posterior aspect of skull at the midline) skull was present here. Physical examination revealed a dark-red, firm mass measuring 5 × 4.5 cm in the posterior aspect of skull. No association with Kasabach- Merritt syndrome (KMS) was observed despite its size. Histologically, KHE was composed of infiltrating nodules with slitlike or crescentic vessels that are poorly canalized and lined by spindled endothelium cells. Immunohistochemically, both spindle and epithelioid cells were immunoreactive for CD34 and CD31, while negative for EMA, cytokeratin or S100 protein. α- SMA were detected in pericytes surrounding spindle cells. Recurrence occurred 2 month after first operation. Wide resection was performed at second operation and the patient was still alive during the 1-year follow- up period.  

Upgrade to premium to download articles

Sign up to access the full text

Already have an account?login

similar resources

kaposifrom hemangioendothelioma of the skull in a 3 year--old boy

kaposiform hemangioendothelioma (khe) appears as a single lesion at birth or early infancy in an equal sex ratio. a rare aggressive vascular proliferation has been recognized as a separate entity from other childhood vascular neoplasm. a 3-year-old iranian boy with a rapidly enlarging mass in his (posterior aspect of skull at the midline) skull was present here. physical examination revealed a ...

full text

Radio-Cytopathological Diagnosis of Eosinophilic Granuloma of Skull in a 13-Year Old Boy

Eosinophilic granuloma is benign end of the spectrum of the Langerhans cell histiocytosis (LCH) which is characterized by solitary or multiple lesions in bones, skin, lung, lymph node etc. Here, we present a case of a 13-year old boy with pain and swelling in the right parietal region of skull with no other complaint. A computerized tomography (CT) scan and subsequent fine needle aspiration cyt...

full text

CARCINOMA OF THE ESOPHAGUS IN A FOURTEEN YEAR OLD BOY

This is the first documented case of esophageal carcinoma in a 14 year old boy which has been reported to date. Carcinoma of the esophagus is rare before the third decade. The present case highlights the fact that the condition should be kept in mind in the differential diagnosis of progressive dysphagia even in children and teenagers

full text

Chronic Recurrent Multifocal Osteomyelitis in a 9-year-old Boy

  Chronic recurrent multifocal osteomyelitis (CRMO) is a rare aseptic, auto-inflammatory bone disorder. CRMO presents with bone pain with or without fever. The diagnosis of CRMO is a diagnosis of exclusion and should be included in the differential diagnosis of chronic inflammatory bone lesions in children. Cultures of the bone are typically sterile, antibiotic therapy does not result in clinic...

full text

Early Puberty in a Two-year-old Boy

Precocious Puberty in a 2-year-old boy  A 2-year-old boy with precocious isosexual matura- (3) Lion is reported.  The pubertal values of serum LH, FSH and Testoste- (4) on and lack of any other pathologic finding were in favour of diagnosis of idiopathic sexual precocity.  The L.R.F. response test was of the adult pattern. The serum LH, FSH and Testosterone decreased following (5) treatment ...

full text

My Resources

Save resource for easier access later

Save to my library Already added to my library

{@ msg_add @}


Journal title

volume 4  issue 3

pages  137- 140

publication date 2009-06-01

By following a journal you will be notified via email when a new issue of this journal is published.

Hosted on Doprax cloud platform doprax.com

copyright © 2015-2023